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KMID : 0363220200580020115
Korean Journal of Dermatology
2020 Volume.58 No. 2 p.115 ~ p.117
Unclassifiable Phakomatosis Pigmentovascularis: A Case Report
Kang In-Jung

Lee Mu-Hyoung
Shin Min-Kyung
Abstract
Phacomatosis pigmentovascularis is a rare syndrome characterized by the association between vascular and extensive pigmentary nevi. In this case, a 4-month-old infant had lesions of the nevus flammeus, lesions of cutis marmorata telangiectatica congenita, and a Mongolian spot. He had no concomitant systemic disease. We herein report a case of unclassifiable phakomatosis pigmentovascularis.
KEYWORD
Cutis marmorata telangiectatica congenita, Mongolian spot, Nevus flammeus, Phakomatosis pigmentovascularis, unclassifiable type
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